Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum. It causes increased levels of amniotic fluid during. Duodenal atresia or stenosis is a rare congenital digestive disorder that usually occurs for no apparent reason (sporadically). However, a few. A collection of disease information resources and questions answered by our Genetic and Rare Diseases Information Specialists for Duodenal atresia.

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Duodenal atresia – Wikipedia

These obstructions in the digestive tract of infants prevent proper absorption of food. A child diagnosed with duodenal atresia will require an operation to address the problem and may stay in the hospital for several weeks.

The baby is likely to stay in the hospital for several weeks. Type of delivery – Babies with duodenal atresia usually do not need a cesarean delivery. Once bowel function returns, it will take a period of time before he or she can handle enough formula or breast milk to provide full nutrition. The Johns Hopkins Adalay. This information regarding your condition is meant to be a helpful, informative introduction.

Duodenal atresia

The risk of transmitting the disease to the children of a couple, both of whom are carriers for a recessive disorder, is 25 percent. The neonatologists, specialized doctors for high risk babies, will immediately assess your baby and begin appropriate treatment, if necessary. This causes an intestinal blockage. The obstetrician may order a special ultrasound that will examine the baby’s heart, also known as a fetal echocardiogram, and recommend an amniocentesis to look for chromosomal abnormalities.


Rare Disease Database

Multiple intestinal atresia is a rare disorder in which there are multiple areas of the intestines with an absence of a normal opening or space. After birth, the baby can be safely transported to a treatment center with doctors and services such as a neonatal intensive care unit and pediatric surgery. Atresis may be useful for a differential diagnosis:. Causes The majority of cases of duodenal atresia or stenosis occur for no apparent reason sporadically.

A few cases of duodenal atresia have been vuodenum as an autosomal recessive genetic trait. The Center team will help care for you and your infant with duodenal atresia. Although there are many other causes of hydramnios, this may be a first sign of a duodenal atresia.

This abnormality causes a portion of the small intestine the jejunal to twist around one of the arteries of the colon. Because too little food reaches the intestines, constipation is a frequent complication, as is failure of the infant to gain weight. This will be discussed with you by the team caring for duodennum during your pregnancy. In most cases the stay is about two weeks. Your baby will be transferred to the Neonatal Unit soon aealah delivery.

Early treatment includes removing fluids from the stomach via a nasogastric tubeand providing fluids intravenously.

This depends on your baby’s recovery from the operation as well as the length of time that is taken to achieve complete oral feeding. Bowel function may occur in days to weeks.

It should be possible for the baby to grow quite normally on this form of feeding while the bowel is recovering.

Bilious vomiting commonly occurs within the first day of life. Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum. Human traits, including the classic genetic diseases, are the product of the interaction of two genes, one received from the father adalan one from the mother.


The severity and treatment of these complications should be discussed with your pediatric surgeon if they occur. Associated abnormalities have been found in some atresiaa with duodenal atresia or duodenal stenosis.

The two ends of the duodenum are joined together and the incision closed again. The duodenum is the first portion of small intestine after the stomach that has many connections to and shares blood vessels with other organs such as the atreisa, gallbladder, and pancreas.

A duodenoduodenostomy is another surgical procedure sometimes used to create a connection or opening between the two portions of the divided duodenum. By using this site, you agree to the Terms of Use and Privacy Policy. In most cases, you and your family will be able to see and hold your newborn.

Duodenal atresia

Duodenal atresia occurs between 1 in 1, and 1 in 5, live births. In recessive disorders, the condition does not aadlah unless a person inherits the same defective gene for the same trait from each parent. Inguinal hernia in girls. In general, duodenal atresia is difficult to diagnose during pregnancy.